Progress heritable soft connective (26 résultats)

Titre: 
Affiner les résultats avec une recherche avancée

Affiner la recherche

  • Livres (26)

à

Fourchette de prix personnalisée (EUR)

à

  • Langue : anglais

    Edité par Cham, Springer International Publishing., 2021

    3030806138 / 9783030806132

    • Couverture rigide

    Vendeur : Universitätsbuchhandlung Herta Hold GmbH, Berlin, AllemagneUniversitätsbuchhandlung Herta Hold GmbH

    Vendeur avec une évaluation de 3 étoiles
    Contacter le vendeur

    Membre d’une association professionnelle : VDAGIAQILAB

    Etat: Occasion

    EUR 22,00

    EUR 30,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 1 disponible

    2nd ed. 2021. IX, 343 p. Hardcover. Einband bestoßen, daher Mängelexemplar gestempelt, sonst sehr guter Zustand. Imperfect copy due to slightly bumped cover, apart from this in very good condition. Stamped. Advances in Experimental Medicine and Biology, 1348. Sprache: Englisch.

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : GreatBookPrices, Columbia, MD, Etats-UnisGreatBookPrices

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Occasion - Comme neuf

    EUR 147,10

    EUR 2,35 expédition 
    Expédition nationale : Etats-Unis

    Quantité disponible : 15 disponibles

    Etat : As New. Unread book in perfect condition.

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : GreatBookPricesUK, Woodford Green, Royaume-UniGreatBookPricesUK

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 139,61

    EUR 17,79 expédition 
    Expédition depuis Royaume-Uni vers Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : New.

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : GreatBookPrices, Columbia, MD, Etats-UnisGreatBookPrices

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 157,47

    EUR 2,35 expédition 
    Expédition nationale : Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : New.

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : Ria Christie Collections, Uxbridge, Royaume-UniRia Christie Collections

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 157,91

    EUR 13,39 expédition 
    Expédition depuis Royaume-Uni vers Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : New. In English.

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : GreatBookPricesUK, Woodford Green, Royaume-UniGreatBookPricesUK

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Occasion - Comme neuf

    EUR 153,99

    EUR 17,79 expédition 
    Expédition depuis Royaume-Uni vers Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : As New. Unread book in perfect condition.

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : AHA-BUCH GmbH, Einbeck, AllemagneAHA-BUCH GmbH

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 144,58

    EUR 35,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 1 disponible

    Taschenbuch. Etat : Neu. Druck auf Anfrage Neuware - Printed after ordering - This volume represents a substantially revised and updated 2nd edition of a reference handbook on major structural components of soft connective tissues and a whole slew of heritable diseases of soft connective tissues. The number of clearly identifiable and distinct disorders has grown somewhat since the 1st edition in 2014, e.g., Ehlers-Danlos syndrome has now 13 entities. A brand new syndrome, Meester Loeys syndrome carrying the name of Bart Loeys was added as a companion to Loeys-Dietz syndrome. Numerous variations of cutis laxa and joint mobility disorders have been discovered taking advantage of recent advancements in genetic analysis. We have acquired better understanding of pathogenesis and biochemical changes in some other, more established entities, such as Marfan and collagen VI myopathies where better management and possible treatment are on the horizon. Even in the case of connective tissue diseases in domestic animals some progress has been made. All these updates werecontributed by a group of distinguished and preeminent physicians and scientists, all of them not just working in the field but making new discoveries described by them.Readers will notice that seemingly there is an overlap among many of these disorders. And indeed, many of them, if not most are interconnected because of the prominent roles of TGFbeta, of fibrillin microfibrils and collagen fibril assembly (and other molecules) playing in connective tissues physiology, and by extension in pathogenesis of many disorders described in the book. What I found particularly helpful that author(s) of each chapter bring their own perspective even when described closely related mechanism of the disease. These observations should help with diagnosis and management of such cases.The first chapters are more general, concentrating more on the physiology, structure and biochemistry of normal soft tissues. That should help in better understanding of the pathophysiology. Last but notleast, the chapters are very readable, more like detective stories than dry description of genetic/biochemical defects. I do hope that basic scientists and clinicians with similar and diverse interests alike will appreciate this volume and will be inspired by it to develop their research in the field. …

  • Autres images

    Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : preigu, Osnabrück, Allemagnepreigu

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 113,20

    EUR 70,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 5 disponibles

    Taschenbuch. Etat : Neu. Progress in Heritable Soft Connective Tissue Diseases | Jaroslava Halper | Taschenbuch | Advances in Experimental Medicine and Biology | ix | Englisch | 2022 | Springer | EAN 9783030806163 | Verantwortliche Person für die EU: Springer Verlag GmbH, Tiergartenstr. 17, 69121 Heidelberg, juergen[dot]hartmann[at]springer[dot]com | Anbieter: preigu.…

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : Books Puddle, Woodside, NY, Etats-UnisBooks Puddle

    Vendeur avec une évaluation de 4 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 189,90

    EUR 3,55 expédition 
    Expédition nationale : Etats-Unis

    Quantité disponible : 4 disponibles

    Etat : New.

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : Revaluation Books, Exeter, Royaume-UniRevaluation Books

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 188,61

    EUR 14,82 expédition 
    Expédition depuis Royaume-Uni vers Etats-Unis

    Quantité disponible : 2 disponibles

    Paperback. Etat : Brand New. 2nd edition. 352 pages. 10.00x7.01x0.74 inches. In Stock.

  • Langue : anglais

    Edité par Palgrave Macmillan, 2022

    3030806162 / 9783030806163

    • Couverture souple

    Vendeur : Buchpark, Trebbin, AllemagneBuchpark

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Occasion

    EUR 98,81

    EUR 105,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 2 disponibles

    Etat : Hervorragend. Zustand: Hervorragend | Seiten: 356 | Sprache: Englisch | Produktart: Bücher | This volume represents a substantially revised and updated 2nd edition of a reference handbook on major structural components of soft connective tissues and a whole slew of heritable diseases of soft connective tissues. The number of clearly identifiable and distinct disorders has grown somewhat since the 1st edition in 2014, e.g., Ehlers-Danlos syndrome has now 13 entities. A brand new syndrome, Meester Loeys syndrome carrying the name of Bart Loeys was added as a companion to Loeys-Dietz syndrome. Numerous variations of cutis laxa and joint mobility disorders have been discovered taking advantage of recent advancements in genetic analysis. We have acquired better understanding of pathogenesis and biochemical changes in some other, more established entities, such as Marfan and collagen VI myopathies where better management and possible treatment are on the horizon. Even in the case of connective tissue diseases in domestic animals some progress has been made. All these updates werecontributed by a group of distinguished and preeminent physicians and scientists, all of them not just working in the field but making new discoveries described by them. Readers will notice that seemingly there is an overlap among many of these disorders. And indeed, many of them, if not most are interconnected because of the prominent roles of TGF¿, of fibrillin microfibrils and collagen fibril assembly (and other molecules) playing in connective tissues physiology, and by extension in pathogenesis of many disorders described in the book. What I found particularly helpful that author(s) of each chapter bring their own perspective even when described closely related mechanism of the disease. These observations should help with diagnosis and management of such cases. The first chapters are more general, concentrating more on the physiology, structure and biochemistry of normal soft tissues. That should help in better understanding of the pathophysiology. Last but notleast, the chapters are very readable, more like detective stories than dry description of genetic/biochemical defects. I do hope that basic scientists and clinicians with similar and diverse interests alike will appreciate this volume and will be inspired by it to develop their research in the field.…

  • Langue : anglais

    Edité par Springer International Publishing, 2021

    3030806138 / 9783030806132

    • Couverture rigide

    Vendeur : AHA-BUCH GmbH, Einbeck, AllemagneAHA-BUCH GmbH

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 190,14

    EUR 35,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 1 disponible

    Buch. Etat : Neu. Druck auf Anfrage Neuware - Printed after ordering - This volume represents a substantially revised and updated 2nd edition of a reference handbook on major structural components of soft connective tissues and a whole slew of heritable diseases of soft connective tissues. The number of clearly identifiable and distinct disorders has grown somewhat since the 1st edition in 2014, e.g., Ehlers-Danlos syndrome has now 13 entities. A brand new syndrome, Meester Loeys syndrome carrying the name of Bart Loeys was added as a companion to Loeys-Dietz syndrome. Numerous variations of cutis laxa and joint mobility disorders have been discovered taking advantage of recent advancements in genetic analysis. We have acquired better understanding of pathogenesis and biochemical changes in some other, more established entities, such as Marfan and collagen VI myopathies where better management and possible treatment are on the horizon. Even in the case of connective tissue diseases in domestic animals some progress has been made. All these updates werecontributed by a group of distinguished and preeminent physicians and scientists, all of them not just working in the field but making new discoveries described by them.Readers will notice that seemingly there is an overlap among many of these disorders. And indeed, many of them, if not most are interconnected because of the prominent roles of TGFbeta, of fibrillin microfibrils and collagen fibril assembly (and other molecules) playing in connective tissues physiology, and by extension in pathogenesis of many disorders described in the book. What I found particularly helpful that author(s) of each chapter bring their own perspective even when described closely related mechanism of the disease. These observations should help with diagnosis and management of such cases.The first chapters are more general, concentrating more on the physiology, structure and biochemistry of normal soft tissues. That should help in better understanding of the pathophysiology. Last but notleast, the chapters are very readable, more like detective stories than dry description of genetic/biochemical defects. I do hope that basic scientists and clinicians with similar and diverse interests alike will appreciate this volume and will be inspired by it to develop their research in the field.…

  • Langue : anglais

    Edité par Springer, 2021

    3030806138 / 9783030806132

    • Couverture rigide

    Vendeur : Books Puddle, Woodside, NY, Etats-UnisBooks Puddle

    Vendeur avec une évaluation de 4 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 252,38

    EUR 3,55 expédition 
    Expédition nationale : Etats-Unis

    Quantité disponible : 4 disponibles

    Etat : New. pp. 343.

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple
    • impression à la demande

    Vendeur : Brook Bookstore On Demand, Napoli, NA, ItalieBrook Bookstore On Demand

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 102,25

    EUR 6,80 expédition 
    Expédition depuis Italie vers Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : new. Questo è un articolo print on demand.

  • Langue : anglais

    Edité par Springer, 2021

    3030806138 / 9783030806132

    • Couverture rigide
    • impression à la demande

    Vendeur : Brook Bookstore On Demand, Napoli, NA, ItalieBrook Bookstore On Demand

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 134,27

    EUR 8,00 expédition 
    Expédition depuis Italie vers Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : new. Questo è un articolo print on demand.

  • Langue : anglais

    Edité par Springer International Publishing, Springer International Publishing Nov 2022, 2022

    3030806162 / 9783030806163

    • Couverture souple
    • impression à la demande

    Vendeur : BuchWeltWeit Ludwig Meier e.K., Bergisch Gladbach, AllemagneBuchWeltWeit Ludwig Meier e.K.

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 128,39

    EUR 23,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 2 disponibles

    Taschenbuch. Etat : Neu. This item is printed on demand - it takes 3-4 days longer - Neuware -This volume represents a substantially revised and updated 2nd edition of a reference handbook on major structural components of soft connective tissues and a whole slew of heritable diseases of soft connective tissues. The number of clearly identifiable and distinct disorders has grown somewhat since the 1st edition in 2014, e.g., Ehlers-Danlos syndrome has now 13 entities. A brand new syndrome, Meester Loeys syndrome carrying the name of Bart Loeys was added as a companion to Loeys-Dietz syndrome. Numerous variations of cutis laxa and joint mobility disorders have been discovered taking advantage of recent advancements in genetic analysis. We have acquired better understanding of pathogenesis and biochemical changes in some other, more established entities, such as Marfan and collagen VI myopathies where better management and possible treatment are on the horizon. Even in the case of connective tissue diseases in domestic animals some progress has been made. All these updates werecontributed by a group of distinguished and preeminent physicians and scientists, all of them not just working in the field but making new discoveries described by them.Readers will notice that seemingly there is an overlap among many of these disorders. And indeed, many of them, if not most are interconnected because of the prominent roles of TGFbeta, of fibrillin microfibrils and collagen fibril assembly (and other molecules) playing in connective tissues physiology, and by extension in pathogenesis of many disorders described in the book. What I found particularly helpful that author(s) of each chapter bring their own perspective even when described closely related mechanism of the disease. These observations should help with diagnosis and management of such cases.The first chapters are more general, concentrating more on the physiology, structure and biochemistry of normal soft tissues. That should help in better understanding of the pathophysiology. Last but notleast, the chapters are very readable, more like detective stories than dry description of genetic/biochemical defects. I do hope that basic scientists and clinicians with similar and diverse interests alike will appreciate this volume and will be inspired by it to develop their research in the field. 356 pp. Englisch.…

  • Langue : anglais

    Edité par Springer International Publishing, 2022

    3030806162 / 9783030806163

    • Couverture souple
    • impression à la demande

    Vendeur : moluna, Greven, Allemagnemoluna

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 107,09

    EUR 48,99 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : New. Dieser Artikel ist ein Print on Demand Artikel und wird nach Ihrer Bestellung fuer Sie gedruckt. Provides an update on the pathophysiology of heritable soft connective tissue diseasesDiscusses the role of individual components of the extracellular matrix of various soft tissue disordersOffers new management options and therapeutic dire.…

  • Langue : anglais

    Edité par Springer, Palgrave Macmillan Nov 2022, 2022

    3030806162 / 9783030806163

    • Couverture souple
    • impression à la demande

    Vendeur : buchversandmimpf2000, Emtmannsberg, BAYE, Allemagnebuchversandmimpf2000

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 128,39

    EUR 60,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 1 disponible

    Taschenbuch. Etat : Neu. This item is printed on demand - Print on Demand Titel. Neuware -This volume represents a substantially revised and updated 2nd edition of a reference handbook on major structural components of soft connective tissues and a whole slew of heritable diseases of soft connective tissues. The number of clearly identifiable and distinct disorders has grown somewhat since the 1st edition in 2014, e.g., Ehlers-Danlos syndrome has now 13 entities. A brand new syndrome, Meester Loeys syndrome carrying the name of Bart Loeys was added as a companion to Loeys-Dietz syndrome. Numerous variations of cutis laxa and joint mobility disorders have been discovered taking advantage of recent advancements in genetic analysis. We have acquired better understanding of pathogenesis and biochemical changes in some other, more established entities, such as Marfan and collagen VI myopathies where better management and possible treatment are on the horizon. Even in the case of connective tissue diseases in domestic animals some progress has been made. All these updates werecontributed by a group of distinguished and preeminent physicians and scientists, all of them not just working in the field but making new discoveries described by them.Readers will notice that seemingly there is an overlap among many of these disorders. And indeed, many of them, if not most are interconnected because of the prominent roles of TGF¿, of fibrillin microfibrils and collagen fibril assembly (and other molecules) playing in connective tissues physiology, and by extension in pathogenesis of many disorders described in the book. What I found particularly helpful that author(s) of each chapter bring their own perspective even when described closely related mechanism of the disease. These observations should help with diagnosis and management of such cases.The first chapters are more general, concentrating more on the physiology, structure and biochemistry of normal soft tissues. That should help in better understanding of the pathophysiology.Last but notleast, the chapters are very readable, more like detective stories than dry description of genetic/biochemical defects. I do hope that basic scientists and clinicians with similar and diverse interests alike will appreciate this volume and will be inspired by it to develop their research in the field.Springer-Verlag KG, Sachsenplatz 4-6, 1201 Wien 356 pp. Englisch.…

  • Langue : anglais

    Edité par Springer, Berlin|Springer International Publishing|Springer, 2021

    3030806138 / 9783030806132

    • Couverture rigide
    • impression à la demande

    Vendeur : moluna, Greven, Allemagnemoluna

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 141,30

    EUR 48,99 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : New. Dieser Artikel ist ein Print on Demand Artikel und wird nach Ihrer Bestellung fuer Sie gedruckt. This volume represents a substantially revised and updated 2nd edition of a reference handbook on major structural components of soft connective tissues and a whole slew of heritable diseases of soft connective tissues.This volume represents a substa.…

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple
    • impression à la demande

    Vendeur : Biblios, frankfurt am main, HESSE, AllemagneBiblios

    Vendeur avec une évaluation de 4 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 183,61

    EUR 9,95 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 4 disponibles

    Etat : New. PRINT ON DEMAND.

  • Langue : anglais

    Edité par Berlin Springer International Publishing Springer Nov 2021, 2021

    3030806138 / 9783030806132

    • Couverture rigide
    • impression à la demande

    Vendeur : BuchWeltWeit Ludwig Meier e.K., Bergisch Gladbach, AllemagneBuchWeltWeit Ludwig Meier e.K.

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 171,19

    EUR 23,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 2 disponibles

    Buch. Etat : Neu. This item is printed on demand - it takes 3-4 days longer - Neuware -This volume represents a substantially revised and updated 2nd edition of a reference handbook on major structural components of soft connective tissues and a whole slew of heritable diseases of soft connective tissues. The number of clearly identifiable and distinct disorders has grown somewhat since the 1st edition in 2014, e.g., Ehlers-Danlos syndrome has now 13 entities. A brand new syndrome, Meester Loeys syndrome carrying the name of Bart Loeys was added as a companion to Loeys-Dietz syndrome. Numerous variations of cutis laxa and joint mobility disorders have been discovered taking advantage of recent advancements in genetic analysis. We have acquired better understanding of pathogenesis and biochemical changes in some other, more established entities, such as Marfan and collagen VI myopathies where better management and possible treatment are on the horizon. Even in the case of connective tissue diseases in domestic animals some progress has been made. All these updates were contributed by a group of distinguished and preeminent physicians and scientists, all of them not just working in the field but making new discoveries described by them.Readers will notice that seemingly there is an overlap among many of these disorders. And indeed, many of them, if not most are interconnected because of the prominent roles of TGFbeta, of fibrillin microfibrils and collagen fibril assembly (and other molecules) playing in connective tissues physiology, and by extension in pathogenesis of many disorders described in the book. What I found particularly helpful that author(s) of each chapter bring their own perspective even when described closely related mechanism of the disease. These observations should help with diagnosis and management of such cases.The first chapters are more general, concentrating more on the physiology, structure and biochemistry of normal soft tissues. That should help in better understanding of the pathophysiology. Last but not least, the chapters are very readable, more like detective stories than dry description of genetic/biochemical defects. I do hope that basic scientists and clinicians with similar and diverse interests alike will appreciate this volume and will be inspired by it to develop their research in the field. 343 pp. Englisch.…

  • Langue : anglais

    Edité par Springer, 2022

    3030806162 / 9783030806163

    • Couverture souple
    • impression à la demande

    Vendeur : Majestic Books, Hounslow, Royaume-UniMajestic Books

    Vendeur avec une évaluation de 4 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 198,26

    EUR 7,71 expédition 
    Expédition depuis Royaume-Uni vers Etats-Unis

    Quantité disponible : 4 disponibles

    Etat : New. Print on Demand.

  • Langue : anglais

    Edité par Springer Netherlands, 2014

    9400778929 / 9789400778924

    Série : Livre 158 sur 544 - Advances in Experimental Medicine and Biology

    • Couverture rigide
    • impression à la demande

    Vendeur : moluna, Greven, Allemagnemoluna

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 181,53

    EUR 48,99 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : Plus de 20 disponibles

    Etat : New. Dieser Artikel ist ein Print on Demand Artikel und wird nach Ihrer Bestellung fuer Sie gedruckt. Provides an update on the pathophysiology of heritable soft connective tissue diseases Discusses the role of individual components of the extracellular matrix in specific aspects of various soft tissue disorders Can be used as a diagnostic .…

  • Langue : anglais

    Edité par Springer, Springer Nov 2021, 2021

    3030806138 / 9783030806132

    • Couverture rigide
    • impression à la demande

    Vendeur : buchversandmimpf2000, Emtmannsberg, BAYE, Allemagnebuchversandmimpf2000

    Vendeur avec une évaluation de 5 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 171,19

    EUR 60,00 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 1 disponible

    Buch. Etat : Neu. This item is printed on demand - Print on Demand Titel. Neuware -This volume represents a substantially revised and updated 2nd edition of a reference handbook on major structural components of soft connective tissues and a whole slew of heritable diseases of soft connective tissues. The number of clearly identifiable and distinct disorders has grown somewhat since the 1st edition in 2014, e.g., Ehlers-Danlos syndrome has now 13 entities. A brand new syndrome, Meester Loeys syndrome carrying the name of Bart Loeys was added as a companion to Loeys-Dietz syndrome. Numerous variations of cutis laxa and joint mobility disorders have been discovered taking advantage of recent advancements in genetic analysis. We have acquired better understanding of pathogenesis and biochemical changes in some other, more established entities, such as Marfan and collagen VI myopathies where better management and possible treatment are on the horizon. Even in the case of connective tissue diseases in domestic animals some progress has been made. All these updates werecontributed by a group of distinguished and preeminent physicians and scientists, all of them not just working in the field but making new discoveries described by them.Readers will notice that seemingly there is an overlap among many of these disorders. And indeed, many of them, if not most are interconnected because of the prominent roles of TGFß, of fibrillin microfibrils and collagen fibril assembly (and other molecules) playing in connective tissues physiology, and by extension in pathogenesis of many disorders described in the book. What I found particularly helpful that author(s) of each chapter bring their own perspective even when described closely related mechanism of the disease. These observations should help with diagnosis and management of such cases.The first chapters are more general, concentrating more on the physiology, structure and biochemistry of normal soft tissues. That should help in better understanding of the pathophysiology.Last but notleast, the chapters are very readable, more like detective stories than dry description of genetic/biochemical defects. I do hope that basic scientists and clinicians with similar and diverse interests alike will appreciate this volume and will be inspired by it to develop their research in the field.Springer-Verlag KG, Sachsenplatz 4-6, 1201 Wien 356 pp. Englisch.…

  • Langue : anglais

    Edité par Springer, 2021

    3030806138 / 9783030806132

    • Couverture rigide
    • impression à la demande

    Vendeur : Majestic Books, Hounslow, Royaume-UniMajestic Books

    Vendeur avec une évaluation de 4 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 265,90

    EUR 7,71 expédition 
    Expédition depuis Royaume-Uni vers Etats-Unis

    Quantité disponible : 4 disponibles

    Etat : New. Print on Demand pp. 343 This item is printed on demand.

  • Langue : anglais

    Edité par Springer, 2021

    3030806138 / 9783030806132

    • Couverture rigide
    • impression à la demande

    Vendeur : Biblios, frankfurt am main, HESSE, AllemagneBiblios

    Vendeur avec une évaluation de 4 étoiles
    Contacter le vendeur

    Etat: Neuf

    EUR 264,83

    EUR 9,95 expédition 
    Expédition depuis Allemagne vers Etats-Unis

    Quantité disponible : 4 disponibles

    Etat : New. PRINT ON DEMAND pp. 343.